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4/2018 vol. 31
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REVIEW
Systemic Sclerosis - Associated Pulmonary Hypertension
Iraklis Tsangaris 1
,
 
Frantzeska Frantzeskaki 1
 
 
 
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2nd Department of Critical Care Medicine and Pulmonary Hypertension Clinic, ATTIKON University Hospital, National and Kapodistrian University of Athens, Chaidari, Greece
 
 
Corresponding author
Iraklis Tsangaris   

2nd Department of Critical Care Medicine and Pulmonary Hypertension Clinic, ATTIKON University Hospital, National and Kapodistrian University of Athens 1 Rimini Str, Chaidari 12462, Greece
 
 
Pneumon 2018;31(4):221-228
 
Article (PDF)
References (47)
 
KEYWORDS
pulmonary hypertension
 scleroderm
 
ABSTRACT
Lung disease is a major complication of systemic sclerosis associated with high morbidity and mortality rates. Pulmonary hypertension and lung fibrosis are the prevalent manifestations of lung disease, usually with overlapping characteristics. A major challenge in the management of the disease, is to identify the phenotypes of patients who might benefit from specific therapeutic modalities. The aim of the present review is to describe the clinical and epidemiological characteristics, classification, risk assessment and management of systemic sclerosis associated pulmonary hypertension.
 
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